Pulmonary Artery Agenesis with Bronchial Asthma

Pulmonary Artery Agenesis with Bronchial Asthma

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Unilateral Pulmonary Artery Agenesis (UPAA) is a rare congenital anomaly during the 4 th week of gestational age.It is defined as an absence of pulmonary parenchyma and its supporting artery.A 9-year-old girl was admitted to our hospital because of chronic cough.

Chest examination showed Oversized Tee a decrement in lung sound of right hemi-thorax with expiratory wheeze.Chest radiography (CXR) revealed a semi-opaque right hemi-thorax.Chest CT with intra-venous contrast demonstrated absence of the right pulmonary artery and lung parenchyma with hyper-inflated left lung and dextro-position of mediastinum.

This Tank Kit case emphasizes that in patients with respiratory compliant and chronic cough CXR must be done to rule out similar diagnosis other than asthma.